Glucose (a type of sugar) is a key source of energy for the body. The body stores glucose as glycogen. Glycogen Storage Disease (GSD) is a condition where the body cannot release glucose from the glycogen stores due to a liver enzyme deficiency. When this happens, the level of glucose in the blood (the blood sugar level) can drop too low. There are eleven different types of GSD which are determined by the part of the body that is affected by the enzyme deficiency. All types of GSD affect the body’s ability to either make or utilize glucose as a form of energy. Source: AGSD
The key to the management of GSD is to maintain normal blood glucose/sugar levels. GSD management varies depending on the type of GSD and the symptoms. A doctor will develop a dietary regimen based on specific symptoms.